JIA classification
Definition of JIA - The term JIA covers a group of diseases, it is a diagnosis of exclusion, with arthritis for six weeks or more, and the cause is unknown - likely a combination of genetic and environmental factors. JIA is rarely familial.
The classification of JIA is essentially based on onset and progression (especially the number of joints affected in the first 6 months), and the presence or absence of rheumatoid factor.
There are several JIA subtypes summarised in the Table below. This knowledge is useful as the JIA subtype broadly determines the management approach.
The classification of Juvenile Idiopathic Arthritis |
|
Characteristic |
Clinical features |
Age at onset |
<16 years |
Minimum duration |
6 weeks |
Subtypes |
|
Systemic |
Arthritis |
Fever, rash, adenopathy, serositis |
|
Oligoarthritis |
• 1–4 joints affected during the first 6 months |
|
|
Polyarthritis |
|
Enthesitis-related∗ arthritis (sometimes called ERA) |
Arthritis and enthesitis, or arthritis or enthesitis with at least two of the following: •Sacroiliac joint tenderness •Inflammatory back pain •HLA B27+ •Family history of HLA B27+ related disease |
Psoriatic arthritis |
Arthritis and psoriasis or arthritis and at least two of: •Dactylitis •Nail changes •Family history of psoriasis |
Undifferentiated |
Arthritis not fulfilling the above categories or fulfilling more than one category |